Shahrekord University of Medical Sciences Journal of Shahrekord University of Medical Sciences 2717-0071 27 3 2025 09 08 Reporting a case of isolated levocardia 142 145 10.34172/jsums.1027 EN Tahereh Heydarian https://orcid.org/0009-0004-1808-4780 Maryam Allahdadian https://orcid.org/0000-0001-5128-9578 Journal Article 10.34172/jsums.1027 2024 10 24 2024 11 16 Isolated levocardia with situs inversus is a rare congenital anomaly characterized by the abnormal positioning of the heart and abdominal organs. This condition is frequently associated with congenital heart defects and typically carries a poor prognosis. Accurate diagnosis and effective management are crucial for improving clinical outcomes. This report presents a case involving a 25-year-old woman in her first pregnancy who underwent a routine ultrasound at 17 weeks and 2 days of gestation. The ultrasound revealed dextrocardia with situs inversus, prompting a referral to a pediatric cardiologist. Subsequent echocardiography at 18 weeks confirmed the presence of the stomach on the right side and a reversed heart axis, leading to a diagnosis of isolated levocardia with atrioventricular septal defects (AVSDs). The pregnancy was medically terminated at 19 weeks, following appropriate medical approval.